Afibrinogenemia
From Health Encyclopedia
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Broader Terms
blood coagulation disorder, genetic disorder
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Facts (generated by robot; please edit if you find it inaccurate)
- Synonyms Congenital Afibrinogenemia Disorder Subdivisions None General Discussion Congenital Afibrinogenemia is a rare disorder characterized by absence of a certain substance (protein) in the blood that is essential in the blood clotting (coagulation) process.
- Afibrinogenemia is the complete absence of fibrinogen.
- Synonyms Congenital AfibrinogenemiaDisorder Subdivisions NoneGeneral Discussion Congenital Afibrinogenemia is a rare disorder characterized by absence of a certain substance (protein) in the blood that is essential in the blood clotting (coagulation) process.
- Increased prothrombin activation in a patient with congenital afibrinogenemia is reversible by fibrinogen substitution.
- Afibrinogenemia is a quantitative deficiency that results in bleeding diatheses.
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