Afibrinogenemia

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Broader Terms

blood coagulation disorder, genetic disorder

Facts (generated by robot; please edit if you find it inaccurate)

  • Synonyms Congenital Afibrinogenemia Disorder Subdivisions None General Discussion Congenital Afibrinogenemia is a rare disorder characterized by absence of a certain substance (protein) in the blood that is essential in the blood clotting (coagulation) process.
  • Afibrinogenemia is the complete absence of fibrinogen.
  • Synonyms Congenital AfibrinogenemiaDisorder Subdivisions NoneGeneral Discussion Congenital Afibrinogenemia is a rare disorder characterized by absence of a certain substance (protein) in the blood that is essential in the blood clotting (coagulation) process.
  • Increased prothrombin activation in a patient with congenital afibrinogenemia is reversible by fibrinogen substitution.
  • Afibrinogenemia is a quantitative deficiency that results in bleeding diatheses.

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