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Obstructive hypertrophy cardiomyopathy is slightly different than the other forms of cardiomyopathy that you may hear about of various platforms. It is a cardiomyopathy that is almost entirely linked with a genetic predisposition compared to other forms of cardiomyopathy linked to alcohol or diabetes. Most of the time, genes will be altered that lead to changes in the muscle of the heart. In a smaller population, this can also be due to long-standing hypertension or simply aging. 

This is a condition that is autosomal dominant. What this means is that if a family member carries one of the two genes for the disease, there is a 75 percent chance that this gene will be passed onto future generations. Because it is autosomal dominant, you only need to have one of these "bad" genes in order to have signs and symptoms of the disease. A family history is a key facet of learning about the possibility of this disease because symptoms are often silent at the start. 

One of the most common presentations of this disease that you will hear about on the news is a young athlete suddenly collapsing and dying during an athletic event. Unfortunately, this is often the case and can leave family members completely blindsided by the suddenness of everything. 

Why this occurs is due to what is happening with the muscles of the heart. As the genes affected lead to slight changes in the musculature, the electrical activity of the heart can be affected substantially. Patients may suffer from heart palpitations in minor cases or ventricular fibrillation in more severe cases that can be fatal. 

Because of the pathology of the disease, the heart is much stiffer and smaller than it normally should be so patients may not be able to pump as much blood as they would normally be able to. As a result, patients may present with symptoms such as dyspnea, fatigue or dizziness. 

Obstructive hypertrophy cardiomyopathy is sometimes caught in young adults when they attempt to pass physical examinations to participate in a sports club.  Doctors should perform at least an EKG to see strange pathological changes in the electrical activity of the heart. What would be best is to order an echocardiogram to ensure that the muscles of the heart are the proper size and that they are working properly. 

Obstructive hypertrophy cardiomyopathy is a condition that requires the most intensive interventions of all the cardiomyopathy possibilities because of how young the patient will be. They will have to withdraw from any sports team and stop strenuous exercise to reduce their chance of ventricular fibrillation. What is more, they will also need to take medications to regulate the rhythm of the heart. 

Even if these may provide temporary relief, most patients will ultimately need to have cardiac surgery to provide the best prognosis. Surgeons may remove part of the damaged cardiac wall, do a cardiac ablation surgery to improve the electrical activity of the heart or implant an ICD pacemaker to help regulate the rhythm of the heart. [1]

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